DOI: https://doi.org/10.22141/2224-0551.2.61.2015.75041

Pathology of the Cardiovascular System in Children with Turner Syndrome

A.Ye. Abaturov, L.L. Petrenko, Ye.A. Agafonova, N.I. Abaturova

Abstract


The paper studies the structure of the pathology of the cardiovascular system in children with Turner syndrome. The results of the survey are based on the findings from 42 patients with Turner syndrome, aged 1.5 to 17 years. It is shown that in 80.9 % of patients with Turner syndrome we have marked pathological changes in the cardiovascular system of varying severity. The most common congenital heart diseases in Turner syndrome are aortic coarctation, bicuspid aortic valve and atrial septal defect. Turner syndrome in 35.6 % of cases is associated with impaired electric work of the heart, in particular, with the long QT syndrome. Atherogenic changes in the lipid profile of patients with Turner syndrome in 21.4 % of cases occur since childhood.


Keywords


Turner syndrome; children; cardiovascular system.

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