Сlinical observation of the child with cystic fibrosis

V.A. Klymenko, O.V. Pasichnyk, N.M. Drobova, K.O. Yanovska


The clinical observation of the child with cystic fibrosis is described in the article. Cystic fibrosis was diagnosed during the neonatal screening. The child received enzyme replacement therapy. Early respiratory disorders (at 3 months of age), airways colonization with Pseudomonas aeruginosa (at 7 months of age), frequent bronchopulmonary exacerbations (pneumonia, bronchiectasis) were characteristic of this clinical case. Antimicrobial treatment was complete only during hospitalization period. But short courses of outpatient prophylactic antimicrobial therapy (because of social aspects) caused the child’s death from pulmonary involvement at the age of 2 years 5 months.


children; cystic fibrosis; lungs disease; Pseudomonas aeruginosa


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